腎臓学と治療学ジャーナル

Mixed Connective Tissue Disorder Associated with Scleroderma Renal Crisis

Abstract

Imran Khan *,Irfan Khan ,Tahir Ahmad ,Huma Noor

Mixed connective tissue disease (MCTD) is a rheumatic disease with a combination of multiple connective tissue disorders, which includes dermatomyositis or polymyositis, systemic sclerosis, systemic lupus erythematosus, rheumatoid arthritis and Sjogren’s syndrome. Renal involvement in mixed connective tissue disorder is a rare occurrence. We present a case of MCTD presenting with SRC managed with ACE Inhibitor (Captopril). The patient had advanced renal failure and presently on maintenance haemodialysis.