血管炎ジャーナル

Large Vessel Vasculitis as a Rare Paraneoplastic Effect of Endometrial Cancer

Abstract

Erin C. Saricilar

A case of large vessel vasculitis as a paraneoplastic syndrome of endometrial cancer is presented which is the first documented case in the literature. Presenting initially as undifferentiated abdominal pain, routine tests presented no clear diagnosis beyond aortitis. PET scan and biopsy showed a non-Mullerian origin endometrial cancer, with the aortitis a likely paraneoplastic syndrome. This syndrome has been demonstrated in other cancers such as myelodysplastic syndromes albeit rarely, but this case opens up differential diagnoses for unexplained large vessel vasculitis cases.