外科ジャーナル

Dyke-Davidoff-Masson Syndrome: A Cause of Recurrent Seizures

Abstract

Bhuria Vandana, Chauhan Meenakshi, Malhotra Vani, Nanda Smiti, Lallar Meenakshi and Jain Shaveta

Objective: Dyke-Davidoff-Masson Syndrome (DDMS) is one of the rare causes of recurrent seizures and can be missed in adults. It is associated with contralateral hemiplegia, mental retardation and facial asymmetry. Confirmed diagnosis can be made with characteristic radiological picture. Hemi-spherectomy is the treatment of choice.

Case: DDMS is usually diagnosed in childhood. Here a rare case of refractory epilepsy is being reported in a 23 years old pregnant woman which was diagnosed as DDMS on radiological findings of cerebral atrophy, ventricle enlargement, dilatation of sulci and osseous hypertrophy of calvarium with increased width of diploic space.

Conclusion: A proper history, thorough clinical examination and characteristic radiological findings provide the correct diagnosis of DDMS. CT/MRI must be performed in patients presenting with recurrent seizures.